Journal of Korean Neurosurgical Society

The Korean Neurosurgical Society (대한신경외과학회)
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A Case of Gliosarcoma Associated with Neurofibromatosis Type 1

제 1 형 신경섬유종증과 동반된 교육종

  • Kim, Dae Won (Department of Neurosurgery, School of Medicine, Wonkwang University) ;
  • Park, Jong Tae (Department of Neurosurgery, School of Medicine, Wonkwang University) ;
  • Kim, Jong Moon (Department of Neurosurgery, School of Medicine, Wonkwang University) ;
  • Kim, Tae Young (Department of Neurosurgery, School of Medicine, Wonkwang University)
  • 김대원 (원광대학교 의과대학 신경외과학교실) ;
  • 박종태 (원광대학교 의과대학 신경외과학교실) ;
  • 김종문 (원광대학교 의과대학 신경외과학교실) ;
  • 김태영 (원광대학교 의과대학 신경외과학교실)
  • Received : 2000.05.26
  • Accepted : 2000.08.14
  • Published : 2001.02.28
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Abstract

A rare case of gliosarcoma with neurofibromatosis type I is presented. The patient was a 33-year-old woman who had headache and vomiting for one week. Multiple neurofibromas over her whole body with many cafeau- lait spots were present since childhood. At admission, she had no focal neurological deficit and ophthalmologic examination revealed bilateral Lisch nodules. Brain CT and MRI revealed a heterogeneously enhancing mass in the left fronto-parietal region with marked peritumoral edema and mass effect. The tumor was removed gross totally and a gliosarcoma was diagnosed histopathologically. Post operative course was uneventful with resolution of symptom, followed by radiotherapy with 60 Gy. A brief overview is given of this rare case together with the pertinent literature.

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