Journal of Korean Neurosurgical Society
- Volume 30 Issue 2
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- Pages.221-226
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- 2001
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- 2005-3711(pISSN)
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- 1598-7876(eISSN)
A Case of Gliosarcoma Associated with Neurofibromatosis Type 1
제 1 형 신경섬유종증과 동반된 교육종
- Kim, Dae Won (Department of Neurosurgery, School of Medicine, Wonkwang University) ;
- Park, Jong Tae (Department of Neurosurgery, School of Medicine, Wonkwang University) ;
- Kim, Jong Moon (Department of Neurosurgery, School of Medicine, Wonkwang University) ;
- Kim, Tae Young (Department of Neurosurgery, School of Medicine, Wonkwang University)
- 김대원 (원광대학교 의과대학 신경외과학교실) ;
- 박종태 (원광대학교 의과대학 신경외과학교실) ;
- 김종문 (원광대학교 의과대학 신경외과학교실) ;
- 김태영 (원광대학교 의과대학 신경외과학교실)
- Received : 2000.05.26
- Accepted : 2000.08.14
- Published : 2001.02.28
Abstract
A rare case of gliosarcoma with neurofibromatosis type I is presented. The patient was a 33-year-old woman who had headache and vomiting for one week. Multiple neurofibromas over her whole body with many cafeau- lait spots were present since childhood. At admission, she had no focal neurological deficit and ophthalmologic examination revealed bilateral Lisch nodules. Brain CT and MRI revealed a heterogeneously enhancing mass in the left fronto-parietal region with marked peritumoral edema and mass effect. The tumor was removed gross totally and a gliosarcoma was diagnosed histopathologically. Post operative course was uneventful with resolution of symptom, followed by radiotherapy with 60 Gy. A brief overview is given of this rare case together with the pertinent literature.