Advances in pediatric surgery

Korean Association of Pediatric Surgeons (대한소아외과학회)
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Mesenchymal Hamartoma of the Liver

간의 중간엽 과오종

  • Huh, Gul (Department of Surgery, Seoul National University College of Medicine) ;
  • Kim, Dae-Yeon (Division of Pediatric Surgery, Asan Medical Center) ;
  • Kim, Ki-Hong (Department of Surgery, Inje University, Ilsan Paik Hospital) ;
  • Jung, Sung-Eun (Department of Surgery, Seoul National University College of Medicine) ;
  • Lee, Seong-Cheol (Department of Surgery, Seoul National University College of Medicine) ;
  • Park, Kwi-Won (Department of Surgery, Seoul National University College of Medicine) ;
  • Kim, Woo-Ki (Department of Surgery, Seoul National University College of Medicine)
  • 허걸 (서울대학교 의과대학 외과학교실) ;
  • 김대연 ;
  • 김기홍 ;
  • 정성은 (서울대학교 의과대학 외과학교실) ;
  • 이성철 (서울대학교 의과대학 외과학교실) ;
  • 박귀원 (서울대학교 의과대학 외과학교실) ;
  • 김우기 (서울대학교 의과대학 외과학교실)
  • Published : 2001.06.30
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Abstract

Mesenchymal hamartoma of the liver is a rare benign tumor, usually presenting in early childhood, Five children with mesenchymal hamartoma of the liver pathologically verified at Seoul National University Children's Hospital between 1978 and 2000 were analyzed retrospectively. There were two girls and three boys, and their mean age at the operation was 16.0months (range, 4-32 months). Three patients presented with abdominal distension. A patient was detected incidentally, and another was detected by prenatal ultrasongraphic examination. Tumor size ranged from $10{\times}8.5cm$ to $34{\times}29cm$. Three tumors were located in the right lobe and two in the left lobe. Four cases underwent complete surgical resection, and the other one underwent incomplete surgical resection and marsupialization. Recurrence or malignant transformation was not noted. Five patients survived without evidence of disease for 35, 36, 38, 142 and 228 months. In conclusion, although mesenchymal hamartoma of the liver is benign lesion. it may be confused. and mixed with embryonal sarcoma. A recent report showed recurrence or malignant transformation after partial excision of the tumor. Therefore. complete excision of the tumor with surrounding normal liver tissue is recommended.

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