Papillary Fibroelastoma Causing Neurologic Symptoms in Patients with Valvular Heart Disease

심장판막질환 환자에서 신경학적 이상을 야기한 유두상 섬유탄력종

  • 강준규 (아주대학교병원 흉부외과학교실) ;
  • 이철주 (아주대학교병원 흉부외과학교실) ;
  • 김재영 (아주대학교병원 흉부외과학교실) ;
  • 홍준화 (아주대학교병원 흉부외과학교실) ;
  • 신준한 (아주대학교병원 순환기내과학교실) ;
  • 김장희 (아주대학교병원 해부병리학교실)
  • Published : 2001.12.01

Abstract

A 43 years old female patient who had been diagnosed as having valvular heart disease but had not received any treatment invited and admitted due to progressive dyspnea. She was diagnosed as having aortic and mitral valve stenosis and regurgitation. Neurologic symptoms developed suddenly therefore, surgery was performed. In the operation field, there were many fungating tissue around the mitral valve annulus and left atrial wall. After operation, no neurologic symptoms were observed and pathologist revealed that fungating tissue was papillary fibroleastoma. The patient recovered and was followed in outpatients department.

본 43세 여환은 심장판막질환으로 진단 받은 후 별다른 치료 없이 지내던 중 내원 전 심해진 호흡곤란으로 입원 치료중 신경학적 이상이 발생되어 중복판막협착 및 폐쇄부전증, 뇌동맥 색전증의 진단 하에 수술 시행하였다. 수술시 좌심실 배부와 승모판막륜 주변에 유두상의 조직들이 다수 발견되었다. 술후 신경학적 이상은 더 이상 보이지 않았고 병리조직학적 검사상 류마치스성 판막소엽에 동반된 유두상 섬유탄력종이 진단되었다. 환자는 수술 후에 잘 회복하였으며, 현재 외래에서 추적 관찰중이다.

Keywords

References

  1. J Am Coll Cardiol v.30 Papillary Fibroelas-toma;Echocardiographic Characteristics for Diagniosis and Pathologic Correlation Kyle WK;Maurice ES;George MG
  2. Heart v.79 Fibroelecstoma;case report and review of the literature A Al-Mohammad;H Pambakian;C Young
  3. Am J Cardiol v.80 Echocardiographic Features of Papillary Fibroelstoma and Their Consequences and Management Henry C Yee;Joel En;Angela D;Mario V
  4. Armed Forces Institute of Pathology Tumors of the heart and great vessels;in;Atlas of Tumor Pathology Third series Burke A;Virmani R
  5. Ann Thorac Surg v.59 Cardiac papillary fibroelstoma Shahian DM;Labib SB;Chang G
  6. Ann Thorac Surg v.52 Primary Cardiac Valve tumors Edward FH;Hale D;Cohen A;Thomson L;Pezzella AT;Virmani R
  7. Chest v.52 Aortic valve papillary fibroelastoma;A diagnosis by transthoracic echocardiogra-phy Gopal A;Li MG;King Dl (et al)
  8. Am Heart J v.126 Diagnosis of papillary fibroelastoma of the mitral valve complicated by non-Q-wave infarction with apical thrombus;transeso-phageal and transthoracic echocardiograpic study Richard J;Castello R;Dressler FA