Journal of Korean Academy of Oral and Maxillofacial Radiology (치과방사선)
- Volume 29 Issue 2
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- Pages.507-521
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- 1999
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- 1225-049X(pISSN)
Osteopetrosis Tards
만발형골화석증
- Kim Young-Hee (Department of Oral and Maxillofacial Radiology Chonnam National University) ;
- Yi Jae-Seo (Department of Oral and Maxillofacial Radiology Chonnam National University) ;
- Yoon Suk-Ja (Department of Oral and Maxillofacial Radiology Chonnam National University) ;
- Kang Byung-Cheol (Department of Oral and Maxillofacial Radiology Chonnam National University)
- 김영희 (전남대학교 치과대학 구강악안면방사선학 교실) ;
- 이재서 (전남대학교 치과대학 구강악안면방사선학 교실) ;
- 윤숙자 (전남대학교 치과대학 구강악안면방사선학 교실) ;
- 강병철 (전남대학교 치과대학 구강악안면방사선학 교실)
- Published : 1999.08.01
Abstract
Osteopetrosis is an uncommon hereditary bone disorder whose prominent radiologic feature characterized by increased bone density. The authors reported a 7-year-old male patient who referred from local dental clinic for dental problems such as early exfoliation of deciduous teeth(#54,73,83) and delayed eruption of permanent teeth(#31.41.36.46). The patient appeared as a poorly developed. Dental X-ray films showed early exfoliation of deciduous teeth, delayed eruption of permanent teeth, and rampant caries. Lateral view of skull demonstrated increased opacity of calvarium, facial bones, and skull base. Generally the skeletal density is greatly increased throughout all bones. Facial CT showed poor development of paranasal sinuses and mastoid air cells. No hematopoietic and neurologic complications such as anemia, thrombocytopenia, blindness and deafness were found. Also mental retardation was not found. The final diagnosis of this case was a osteopetrosis tarda. Sometimes patient with osteopetrosis tarda may be developed dental problems prior to severe systemic symptoms. The dentist can be the first clinician to see the patient. It is very important for the dentist to have the knowledge of the osteopetrosis and to care the patient's dental problems to prevent complication such as osteomyelitis of jaws.