Childhood Kidney Diseases

Korean Society of Pediatric Nephrology (대한소아신장학회)
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A Case of Infantile Nephrotic Syndrome with Focal Segmental Glomerulosclerosis

국소성 분절성 사구체 경화증에 의한 영아형 신증후군 1례

  • Kim Se Eun (Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine) ;
  • Han Young Sim (Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine) ;
  • Song Min Seop (Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine) ;
  • Chung Woo Yeong (Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine)
  • 김세은 (인제대학교 의과대학 부산백병원 소아과학교실) ;
  • 한영심 (인제대학교 의과대학 부산백병원 소아과학교실) ;
  • 송민섭 (인제대학교 의과대학 부산백병원 소아과학교실) ;
  • 정우영 (인제대학교 의과대학 부산백병원 소아과학교실)
  • Published : 1999.05.01
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Abstract

Focal Segmental Glomerulosclerosis(FSGS) is one of the underlying pathology of congenital and infantile nephrotic syndrome. There is no ultimate curative treatment except renal transplantation. We have experienced a case of infantile nephrotic syndrome In a 10 month old boy who presented with proteinuria and hematuria. His elder brother also suffered from nephrotic syndrome and died at the age of 18 months due to sepsis. We have diagnosed this patient with clinical manifestations, laboratory data and pathologic findings which was done by open renal biopsy. The patient expired 54 days after admission because or progressive uremia and sepsis.

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