Congenital Hemihypertrophy of Upper Extremity (A Case Report)

좌측상지에 발생한 선천성편비대 1례보고(증례보고)

  • Choi Chang-Hyuk (Department of Orthopaedic Surgery, School of Medicine, Catholic University of Taegu-Hyosung) ;
  • Kwun Koing-Woo (Department of Orthopaedic Surgery, School of Medicine, Catholic University of Taegu-Hyosung) ;
  • Kim Shin-Kun (Department of Orthopaedic Surgery, School of Medicine, Catholic University of Taegu-Hyosung) ;
  • Lee Sang-Wook (Department of Orthopaedic Surgery, School of Medicine, Catholic University of Taegu-Hyosung) ;
  • Kim Kyung-Ho (Department of Orthopaedic Surgery, School of Medicine, Catholic University of Taegu-Hyosung) ;
  • Park Jae-Bok (Department of Pathology, School of Medicine, Catholic University of Taegu Hyosung)
  • 최창혁 (대구효성가톨릭대학교 의과대학 정형외과학교실) ;
  • 권굉우 (대구효성가톨릭대학교 의과대학 정형외과학교실) ;
  • 김신근 (대구효성가톨릭대학교 의과대학 정형외과학교실) ;
  • 이상욱 (대구효성가톨릭대학교 의과대학 정형외과학교실) ;
  • 김경호 (대구효성가톨릭대학교 의과대학 정형외과학교실) ;
  • 박재복 (대구효성가톨릭대학교 의과대학 병리학교실)
  • Published : 1998.03.01

Abstract

This report describes a rare, congenital hypertrophy of the left upper extremity that appeared after compressive bandage of right arm at the age of two. He is eighteen years old, and hypertrophy was aggravated for about 2 years since he started weight training exercise. Recently, skin turgor changed and he visited the Dermatology department. Skin biopsy revealed increased thickness of the dermis. On Orthopaedic examination, the left arm showed non­specific neuro-muscular changes other than easy fatigability a.nd increased skin consistency after exercise, compared to the right arm. The differences of circumference were 2.5 to 4cm according to the level of the upper limb. But the relative proportion of hypertrophy of the limb was balanced., On X-ray examination, bony changes were not shown. Through the MRI, we could find edematous changes of subcutaneous fatty tissue. Muscular structures showed unremarkable changes. Through the endurance test of both arms, we could find a decrease in endurance of the left upper arm musculatures. On histologic examination, infrequent focal necrosis and peri fascicular degeneration of the muscle fiber were present.

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