Poland Syndrome -One Case Report-

폴란드 증후군 -1례 보고-

  • Shin, Sung-Ho (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University Hospital) ;
  • Chon, Yang-Bin (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University Hospital) ;
  • Chon, Soon-Ho (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University Hospital) ;
  • Kang, Jung-Ho (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University Hospital) ;
  • Kim, Hyuk (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University Hospital) ;
  • Chung, Won-Sang (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University Hospital) ;
  • Kim, Young-Hak (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University Hospital) ;
  • Jee, Heng-Ok (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University Hospital)
  • 신성호 (한양대학교병원 흉부외과학교실) ;
  • 전양빈 (한양대학교병원 흉부외과학교실) ;
  • 전순호 (한양대학교병원 흉부외과학교실) ;
  • 강정호 (한양대학교병원 흉부외과학교실) ;
  • 김혁 (한양대학교병원 흉부외과학교실) ;
  • 정원상 (한양대학교병원 흉부외과학교실) ;
  • 김영학 (한양대학교병원 흉부외과학교실) ;
  • 지행옥 (한양대학교병원 흉부외과학교실)
  • Published : 1998.09.01

Abstract

The chest wall deformity associated with Poland's syndrome is a very rare anomaly which consists of congenital unilateral absence of the sternal head of the pectoralis major muscle and various abnormalities of the upper extremity. Other clinical features associated with Poland's syndrome include deficiency or absence of the breast and nipple, deficiency of subcutaneous fat and axillary hair, and abnormalities of costal cartilages and anterior ends of ribs. The origin remains uncertain, but is considered not to be hereditary. Poland's syndrome may pose a serious psychologic and cosmetic problem, early recognition and surgical correction may prove beneficial. A 37 year old patient with Poland's syndrome was encountered and underwent satisfactory surgical correction.

Poland씨 증후군과 관련된 흉벽기형은 매우 드문 질환으로 선천적으로 대흉근의 흉골부 결손과 한쪽 상지의 다양한 기형을 동반한다. 또한 Poland씨 증후군의 다른 임상적 특징은 유방과 유두의 결손 및 저형성, 피하 지방과 액모의 결손, 늑연골 및 늑골전면부의 이상을 포함한다. 그 기원은 확실하지 않으나 유전과는 관계 가 없는 것으로 알려져 있다. Poland씨 증후군은 심한 정신적인 그리고 신체적인 문제를 일으킬 수 있으며 초기 발견 및 수술적 교정이 이득이 될 것으로 생각된다. 본원은 Poland씨 증후군으로 진단된 37세 남자환자를 성공적으로 수술치험하였기에 이를 보고하는 바이다.

Keywords

References

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