Tuberculosis and Respiratory Diseases
- Volume 44 Issue 5
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- Pages.1184-1193
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- 1997
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- 1738-3536(pISSN)
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- 2005-6184(eISSN)
A Case of Pulmonary Lymphangioleiomyomatosis Associated with Tuberous Sclerosis and Renal Angiomyolipoma
결절성 경화증과 동반된 폐의 임파관평활근종증 1예
- Baik, Jung-Min (Department of Internal Medicine, Nowon Eulji Medical Center) ;
- Hong, Han-Ki (Department of Internal Medicine, Nowon Eulji Medical Center) ;
- Oh, Young-Bae (Department of Internal Medicine, Nowon Eulji Medical Center) ;
- Lee, Sang-Moo (Department of Internal Medicine, Nowon Eulji Medical Center) ;
- Park, Man-Sil (Department of Chest Surgery, Nowon Eulji Medical Center) ;
- Yoo, Tak-Keun (Department of Urology, Nowon Eulji Medical Center) ;
- Ko, Eun-Joo (Department of Radiology, Nowon Eulji Medical Center) ;
- Kim, Eun-Kyung (Department of Anatomical Pathology, Nowon Eulji Medical Center)
- 백정민 (노원을지병원 내과) ;
- 홍한기 (노원을지병원 내과) ;
- 오영배 (노원을지병원 내과) ;
- 이상무 (노원을지병원 내과) ;
- 박만실 (노원을지병원 흉부외과) ;
- 유탁근 (노원을지병원 비뇨기과) ;
- 고은주 (노원을지병원 진단방사선과) ;
- 김은경 (노원을지병원 해부병리과)
- Published : 1997.10.31
Abstract
Lymphangioleiomyomatosis(LAM) is rare and essentially limited to women in the reproductive ages. A 39-year-old female was admitted due to progressive exertional dyspnea and intermittent productive cough. Chest PA showed marked hyperinflation of the lung associated with a diffuse reticulo-nodular pattern. High resolution CT scan of the thorax demonstrated that diffusely scattered thin-walled cysts were distributed throughout the bilateral lung fields. Abdominal CT scan showed variable sized multiple angiomyolipoma of both kidney. By open lung biopsy, she was diagnosed as pulmonary LAM associated with Tuberous sclerosis and renal Angiomyolipoma. We present the case and discuss the connection between pulmonary LAM and Tuberous sclerosis.
저자들은 결절성 경화증과 동반된 폐의 임파관평활근종증 1예를 경험하였기에 증례와 함께 결절성 경화증과 폐의 임파관평활근종증과의 관계를 문헌고찰과 함께 보고하는 바이다.