Tuberculosis and Respiratory Diseases
- 제44권4호
- /
- Pages.935-941
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- 1997
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- 1738-3536(pISSN)
- /
- 2005-6184(eISSN)
자연소실의 경과를 보인 특발성 종격동 섬유화증 1예
A Case of Spontaneous Resolution of Idiopathic Mediastinal Fibrosis
- 왕준호 (건국대학교 의과대학 내과학교실) ;
- 송광선 (연세대학교 원주의과대학 내과학교실) ;
- 김현준 (건국대학교 의과대학 내과학교실) ;
- 송기호 (건국대학교 의과대학 내과학교실) ;
- 인행환 (건국대학교 의과대학 내과학교실) ;
-
최수봉
(건국대학교 의과대학 내과학교실)
;
- 조미연 (연세대학교 원주의과대학 병리학교실) ;
- 성기준 (연세대학교 원주의과대학 방사선과교실) ;
- 신계철 (연세대학교 원주의과대학 내과학교실)
- Wang, Joon-Ho (Department of Internal Medicine, Kon-Kuk University College of Medicine) ;
- Song, Kwang-Seon (Department of Internal Medicine, Yonsei University Wonju, College of Medicine) ;
- Kim, Hyun-Jun (Department of Internal Medicine, Kon-Kuk University College of Medicine) ;
- Song, Ki-Ho (Department of Internal Medicine, Kon-Kuk University College of Medicine) ;
- In, Haing-Hwan (Department of Internal Medicine, Kon-Kuk University College of Medicine) ;
-
Choi, Su-Bong
(Department of Internal Medicine, Kon-Kuk University College of Medicine)
;
- Joo, Mi-Yeun (Department of Pathology, Yonsei University Wonju College of Medicine) ;
- Sung, Ki-Joon (Department of Radiology, Yonsei University Wonju College of Medicine) ;
- Shin, Kye-Chul (Department of Internal Medicine, Yonsei University Wonju, College of Medicine)
- 발행 : 1997.08.31
초록
저자들은 흉통을 주소로 내원한 53세 남자 환자에서 특발성 종격동 섬유증 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.
Mediastinal fibrosis is pathologically characterized by chronic inflammation and fibrosis of mediastinal soft tissue. Mediastinal fibrosis is local expression of a family of systemic fibrosing syndroms. This can result in compression of adjacent mediastinal structures. Idiopathic fibrosing syndromes include retroperitoneal fibrosis, sclerosing cholangitis of the orbit and fibrosis of the thyroid gland(Riedel's struma). The cause of these disorders is obscure, in some instance there is an underlying malignancy, infection, history of drug ingestion, or trauma with retroperitoneal bleeding. Treatment of mediastinal fibrosis depends on structures involved by the fibrotic process. The disease is self limited in most case or improved by steroids uses. We experienced a case of idopathic sclerosing mediastinitis with orbital fibrous dysplasia of unknowm cause, which was confirmed by open lung biopsy, so reported it with a review of literature.