A Clinical Experience of Neurofibromatosis Involving Periorbital Region

안와부위에 발생한 신경섬유종증의 임상적 치험례

  • Park Dae-Hwan (Department of Plastic and Reconstructive Surgery College of Medicine, Catholic University of Taegu Hyosung) ;
  • Kim Tae-Mo (Department of Plastic and Reconstructive Surgery College of Medicine, Catholic University of Taegu Hyosung) ;
  • Han Dong-Gil (Department of Plastic and Reconstructive Surgery College of Medicine, Catholic University of Taegu Hyosung) ;
  • Ahn Ki-Young (Department of Plastic and Reconstructive Surgery College of Medicine, Catholic University of Taegu Hyosung)
  • 박대환 (대구효성가톨릭대학교 의과대학 성형외과학교실) ;
  • 김태모 (대구효성가톨릭대학교 의과대학 성형외과학교실) ;
  • 한동길 (대구효성가톨릭대학교 의과대학 성형외과학교실) ;
  • 안기영 (대구효성가톨릭대학교 의과대학 성형외과학교실)
  • Published : 1997.05.01

Abstract

Neurofibromatosis, now termed neurofibromatosis type I, is known as a congenital and familial disease presenting abnormalities of the skin, nervous system, bones, and soft tissue. We experienced a case of extremely large neurofibromatosis which developed on the orbital and temporal region of a 24-year-old man. The tumor was widely excised including normal skin margin, outer table of cranium, a part of zygoma and maxilla. Bony defect was reconstructed by rib bone graft and secondary cosmetic correction of blepharoptosis was performed using supratarsal fixation in postoperative 6 months.

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