$CO_2$Laser Aryepiglottoplasty for Treatment of Laryngomalacia in Patau Syndrome

PATAU 증후군에 동반된 후두연화증의 $CO_2$LASER를 이용한 수술치험례

Laryngomalacia is the most common cause of stridor in infant. It is a relatively benign self-limiting condition, but in severe cases, it results in obstructive sleep apnea, cor pulmonale , gastroesophageal reflux, failre to thrive, pectus excavatum, respiratory failure and death. When the airway obstruction related to laryngomalacia becomes significant, surgical correction of the underlying laryngeal deformity is indicated. Numerous reports provide evidence to support the trimming supraglottic soft tissue by using either conventional instruments or the surgical laser for treatment of severe laryngomalacia. Recently, authors experienced a case of laryngomalacia with Trisomy 13 (Patau syndrome) which had three times respiratory arrest and was treated with laser aryepiglottoplasty. We report this case with review of the literatures.

저자들은 Patau증후군에 동반된 후두연화증으로 심폐정지가 유발된 환아에서 $CO_2$레이저를 이용한 aryepiglottoplasty를 시행하여 극적인 호전을 보였기에 문헌고찰과 함께 치료경험을 보고하는 바이다.