Primary Pulmonary Artery Sarcoma A Case Report -A Case Report-

원발성 폐동맥 육종

  • 김성완 (고려대학교 의과대학부속 안암병원 흉부외과 교실) ;
  • 구본원 (고려대학교 의과대학부속 안암병원 흉부외과 교실)
  • Published : 1997.10.01

Abstract

Primary pulmonary artery sarcoma is a rare tumor and commonly misdiagnosed as pulmonary embolism. The prognosis of these tumors is very poor. The Median length of survival without surgical resection is approximately 1.5 months, but surgical resection has lengthened survival time to approximately 1 year. We encountered a case of primary pulmonary artery sarcoma, with a 55 year-old woman whose symptoms were exertional dysp ea, right chest pain, and hemoptysis. A preoperative chest CT scan revealed mass lesion mimicking pulmonary embolism. Pulmonary angioplasty and right Pneumonectomy were Performed on partial cardiopulmonary bypass. Postoperatively the mass was confirmed as undifferenciated sarcoma histopathologically. The symptoms were somewhat improved, but the patient died of unknown causes about 3 months after surgery.

원발성 폐동맥 육종은 드물며, 흔히 폐동맥 색전증으로 오진하기 쉽다. 예후는 매우 좋지않아서 치료하지 않았을 때의 생존율이 약 1.5개월이며,수술후에도 생존율을 일년정도까지 연장할 수있다. 본 교실에서는 원발성 폐동맥 육종을 1례 치험하였기에 보고하고자 한다. 환자는 55세 여자로 주증상은 호흡곤란, 우측흉통, 및 객혈이었다. 술전 흉부 전산화단층촬영상 폐동맥 색전증과 유사한 종괴음영을 나타내었다. 수술은 부분 체외순환하에 폐동맥 성형술과 우측전폐 절제술이 시행되었다. 술후 조직학적 진단은 미분화 육종이었고, 증상은 다소 호전되었으나 술후 3개월에 원인 미상으로 사망하였다.

Keywords

References

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