A Case of Biphasic Pulmonary Blastoma

이상성(Biphasic) 폐 모세포종 1예

  • Kim, Byoung Hun (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Jeon, Seok Hoon (Department of Pathology, College of Medicine, Hanyang University) ;
  • Lee, Kyung Sang (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Yang, Suck Chul (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Yoon, Ho Joo (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Shin, Dong Ho (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Kim, In Soon (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Park, Sung Soo (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Lee, Jung Hee (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Park, Chan Kum (Department of Pathology, College of Medicine, Hanyang University) ;
  • Lee, Joong Dal (Department of Pathology, College of Medicine, Hanyang University)
  • 김병훈 (한양대학 의과대학교 내과학 교실) ;
  • 전석훈 (한양대학 의과대학교 병리학 교실) ;
  • 이경상 (한양대학 의과대학교 내과학 교실) ;
  • 양석철 (한양대학 의과대학교 내과학 교실) ;
  • 윤호주 (한양대학 의과대학교 내과학 교실) ;
  • 신동호 (한양대학 의과대학교 내과학 교실) ;
  • 김인순 (한양대학 의과대학교 내과학 교실) ;
  • 박성수 (한양대학 의과대학교 내과학 교실) ;
  • 이정희 (한양대학 의과대학교 내과학 교실) ;
  • 박찬금 (한양대학 의과대학교 병리학 교실) ;
  • 이중달 (한양대학 의과대학교 병리학 교실)
  • Published : 1996.10.30

Abstract

Pulmonary blastoma is a primary lung tumor consisting of a mixture of immature embryonal-like mensenchymal and epithelial components and in some areas resemble embryonal lung tissue of up to 3-4 months gestational age. The tumor was first described in 1945 by Barren and Barmard and again in 1952 by Barmard, who named it an embryoma of the lung which resembled fetal lung histologically, with glandular structures lined by non-ciliated epithelium and a surrounding stroma resembling mesenchyme. In 1961 Spencer renamed them Pulmonary blastoma as he believed they represented neoplasms similar in pathogenesis to nephroblastoma. The prognosis of these rumors is poor, and the clinical course is not readily predicted from histological appearance. Untill now, more than one hundred cases have been reponed in the literature in the word and there is no report in Korea. We report a case of biphasic pulmonary blastoma, which ruptured spontaneously, in a 31-year-old young man who was presented as sharp pain under the right subscapular area.

폐 모세포종은 미숙한 간엽 혹은 형태학적으로 태생기 3-4개월의 폐 구조와 유사한 상피세포로 구성된 폐종양의 하나이다. 저자들은 외적 자극없이 저절로 파열된 이상성 폐 모세포종 1예를 경험하였기에 보고 하는 바이다.

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