신경섬유종증을 동반한 신경성 육종과 흉강내 뇌척수막류의 치험 1례

Surgical Treatment of "Dumb-bell" Neurosarcoma and Intrathoracic Meningocele Associated with Von Recklinghausen`s Disease -A case report-

  • 발행 : 1995.10.01

초록

Neurosarcoma is relatively rare, but is seen frequently in association with stigmata of neurofibromatosis ie., Cafe au lait pigmentation and cutaneous neurofibromatosis. Both advanced age and association with neurofibromatosis increase the likelihood of malignant degeneration to neurosarcoma. It also may be dumb bell-shaped with intraspinal extension. Thoracic meningocele is rare and represents a protrusion of the dural sac through an abnormally large or malformed intervertebral foramen. The patient is usually asymptomatic, with evidence of paravertebral mass on the chest rentgenogram. In one operation we removed a "Dumb-bell" neurosarcoma and intrathoracic meningocele in a 52 year old woman using a cervical laminectomy with a trap-door incision. She was discharged at 17 days after the operation with a sequelae of excision of nerve roots C8 and T1. Postoperative radiation therapy was performed during the follow-up period.up period.

키워드

참고문헌

  1. Mayo Clin Proc v.53 Dumbbell neurogenic tumor of the mediastinum Akawari,O.E.;Payne,W.S.;Onofrio,B.N.(et al.)
  2. Surg Gynecol Obstet v.94 Dumbbell (hourglass) neuroblastomas affecting the spinal cord Dodge,H.W.(Jr);Love,J.G.
  3. Ann Thorac Surg v.17 Neurogenic tumors of the mediastinum Gale,A.W.;Jelihovsky,T.;Grant,A.F.;Lekcie,B.D.;Nicks,R.
  4. Thorax v.33 Intrathoracic tumors Davidson,K.G.;Walbaum,P.R.;Mccormack,J.M.
  5. Am J Roentgenol v.159 Intrathoracic neurogenic tumors : MR-pathologic correlation Sakai,F.
  6. Ann Thorac Surg v.36 Combined approach to "dumbbell" intrathoracic and intraspinal neurogenic tumors Grillo,H.C.;Ojeman,R.E.;Grigo,K.M.(et al.)
  7. Mediastinal Surgery Benign and malignant neurogenic tumors of the mediastinum in adults Shields,T.W.;Shilds,T.W.(ed.)
  8. J Jpn Assoc Chest Surg v.7 Thoracoscopic surgery for chest wall, pleural and mediastinal tumors Higashima,M.