Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
권호 표지

Congenital Supravalvular Aortic Stenosis Associated with Williams'Syndrome -One Case Report-

Williams' syndrome을 동반한 선천성 대동맥 판상협착 -치험 1례-

  • Published : 1995.04.01
Download PDF
⟨ Previous Next ⟩

Abstract

We expericenced one case of surgical treatment of congenital supravalvular aortic stenosis associated with Willjams` syndrome using Dory procedure. A 22 years-old male patient was admitted to the cardiology department due to dyspnea,easy fatigue,dizziness. On physical examination,systolic murmur was audibled at fight second parasternal intercostal space and his general appearance was elfin face and mental retardation was noted. Cardiac catheterization was revealed as a supravalvular aortic stenosis and pressure gradient was 45mmHg between the left ventricle and the aorta. Successful surgical treatment was accomplished with Inverted Y procedu~:e using Dacron patch[Doty procedure . Postoperative course was uneventful and he was discharged in good condition.

Keywords

References

  1. J Thorac Cardiovasc Surg v.105 Result of surgical repair of congenital supravalvular aortic stenosis Myers,J.L.;Waldhausen,J.A.;Cyran,S.E.(et al.)
  2. Ann Thorac Surg v.46 Extended aortoplasty to relieve supravalvular aortic stenosis Stewart,S.;Alexson,C.;Manning,J.
  3. Ann Thorac Surg v.45 Surgical spectrum of aortic stenosis in children : a thirty-year experience with 257 children Brown,J.W.;Stevens,L.S.;Holly(et al.)
  4. Am J Cardiol v.51 Supravalvular aortic stenosis : a 20-year clinical perspective and experience with patch aortoplasty Flaker,G.;Teske,D.;Kilman,J.;Hosier,D.;Wooley,C.
  5. Am J Cardiol v.37 Result of surgery for congenital supravlvular aortic stenosis Weisz,D.;Hartmann,A.F.;Weldon,C.S.
  6. J Thorac Cardiovasc Surg v.74 Supravalvular aortic stenosis Doty,D.B.;Polansky,D.B.;Jenson,C.B.
  7. J Thorac Cardiovasc Surg v.51 Surgical treatment of supravalvular aortic stenosis : a report of 16 cases and review of the literature Rastelli,G.C.;McGoon,D.C.;Ongley,P.A.(et al.)
  8. J Thorac Cardiovasc Surg v.41 The Surgical Treatment of supravalvular aortic stenosis McGoon,D.C.;Mankin,H.T.;Vlad,P.(et al.)