A REPORT OF THREE CASES OF NEUROFIBROMATOSIS IN THE HEAD

두부에 발생한 신경섬유종증의 증례보고

  • Shin In-Sook (Dept. of Dental Radiology, College of Dentistry, Yonsei University) ;
  • Cho Jeong-Shin (Dept. of Dental Radiology, College of Dentistry, Yonsei University) ;
  • Lee Jang Yeol (Dept. of Dental Radiology, College of Dentistry, Yonsei University) ;
  • Go Jee Young (Dept. of Dental Radiology, College of Dentistry, Yonsei University) ;
  • Kim Sun-Yong (Dept. of Dental Radiology, College of Dentistry, Yonsei University) ;
  • Park Chang-Seo (Dept. of Dental Radiology, College of Dentistry, Yonsei University) ;
  • Kim Kee Deog (Dept. of Dental Radiology, College of Dentistry, Yonsei University)
  • 신인숙 (연세대학교 치과대학 치과방사선학교실) ;
  • 조정신 (연세대학교 치과대학 치과방사선학교실) ;
  • 이장렬 (연세대학교 치과대학 치과방사선학교실) ;
  • 고지영 (연세대학교 치과대학 치과방사선학교실) ;
  • 김선용 (연세대학교 치과대학 치과방사선학교실) ;
  • 박창서 (연세대학교 치과대학 치과방사선학교실) ;
  • 김기덕 (연세대학교 치과대학 치과방사선학교실)
  • Published : 1994.06.01

Abstract

Neurofibromatosis, or Von Recklinghausen's disease is inhereted as an autosomal dominent neurocutaneous systemic disease. It is characterized by multiple Cafe-au-lait spots, generlaized cutaneous neurofibromas. It affects one in 3000 births. We observed the clinical, radiologic and histopathologic findings of 3 cases of neurofibromatosis and obtained following results. 1. All patients had multiple Cafe-au-lait spots and neufibromas. 2. Two patients had radiographic changes of pressive erosion and mesodermal dysplasia. 3. Two patients had plexiform neurofibromas and 1 patient had diffuse neurofibromas. Conclusively, we classified these 3 cases as NF-I.

Keywords