A CASE OF NARCOLEPSY IN A 11 YEAR-OLD BOY

소아 기면증 1예

Narcolepsy's age at onset is reported to be relatively homogeneous, occuring usually after the onset of puberty, although most cases are diagnosed when the patients are in their late teens to late 20s. It is very unusual for a patient to develop narcolepsy before 15 years of age or after 30 years of age. A 11-year old boy who has developed excessive daytime sleepiness since age of 7 and has all the four major features of narcolepsy by the time of evaluation is presented. On polysomnographic examination, the patient showed two sleep onset REM periods in the three latency test of the multiple sleep latency test and the nocturnal polysomnogram. In addition, the findings of typing HLA class I and II of the patient's family are presented. Reports of pediatric narcolepsy previously reported are reviewed.

기면증의 초발연령은 비교적 균일하여 15세 이전, 보통 30세이후에 발병하는 것으로 알려져있다. 저자는 기면증의 4대 증상인 주간의 과도한 졸리움, 탈력 발작, 수면마비 및 입면환각을 보이며 수면다원 검사에 의해 진단된 11세 남아를 경험하였기에 문헌고찰과 함께 이를 보고하고자 한다.