태아에서 발생한 Cariac Rhabdomyoma 치험 1례

Cardiac Rhabdomyoma in Neonate; A Case Report

  • 발행 : 1993.10.01

초록

We experienced a case of cardiac rhabdomyoma,which is incidentally found at perinatally checked sonography.The cardiac rhabdomyoma is the most common cardiac tumor of infants & children, and second most common cardiac tumor of all age groups, which is usually multiple in the case of 90%, invariably involves the ventricles affecting the left & right side equally. In more than fifty percents, the size of cardiac rhabdomyoma is enough large to threatening the life of newborn within 24hrs of birth. Cardiac rabdomyoma is actually a myocardial harmatoma rather than a true neoplasm,because of the finding of complete lack of mitotic activities. Recently,more advanved instruments such as ultrasonography or echocardiography allows to us early detection & surgical intervention of this tumor. In our case, the tumor was found at both ventricles, which occupied nearly total chambers of both ventricles. The patient was operated on 3 day after birth. The operation was removal of the tumor through left ventriculotomy and right ventriculotomy respectively. He expired in the immediate postoperative period due to low cardiac output syndrome, despite of massive inotropic agents.

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참고문헌

  1. J Thorac cardiovasc Surg v.87 Cardiac rhabdomyoma surgical treatment in the neonate. Corno,A.;Simone,G.;Catena,G.;Marcelletti,C.
  2. Am J cardiol. v.66 Natural history of cardiac rhadbomyoma in infancy and childhood. Smythj,J.F.;Dyck,J.D.;Smalhorn,J.F.;Freedom,R.M.
  3. Am J Cardiol v.30 Clinical presentation of the heart tumor in the infancy and childhood. Shaher,R.M.;Minster,J.;Farina,M.;Alley,R.;Bishop,M.
  4. Am J Cardiol v.38 Cardiac rhabdomyoma a clinicopathologic and electron microscopic study. Fenoglio,J.J.;McAllister,H.A.;Ferrans,V.
  5. Am J Medical Genetics. v.42 Incidence of tuberous sclerosis in patients with cardiac rhabomyoma. Webb,D.W.;Osborne,J.P.
  6. Am J of cardiol. Spontaneous regression of cardiac rhabdomyoma. Farooki,Z.Q.;Ariciniegas,E.;Hakimi,M.;Truccune,N.J.;Green,E.W.