폐동맥 폐쇄, 심실중격 결손, 동맥관 개존 및 심방중격 결손을 동반한 선천성 교정형 대동맥 전위증의 치험

Congenitally Corrected Transposition of the Great Arteries [SLL] with Pulmonary Atresia, Ventricular Septal Defect,Patent Ductus Arteriosus, and Atrial Septal Defect -One case report-

Congenitally corrected transposition of the great arteries is a rare congenital heart anomaly, in isolation, has no hemodynamic consequences. It is usually associated with one or more of a variety of intracardiac lesions, ventricular septal defect, valvular or subvalvular pulmonary stenosis, and deformity of the systemic atrioventricular valve with insufficiency. This report describes a successful two stage operation for congenitally corrected transposition, [SLL] type, with ventricular septal defect, pulmonary atresia, persistent ductus arteriosus, and atrial septal defect. A 9 years old patient underwent modified Blalock-Taussig operation because of severe pulmonary hypoplasia. 2 years later a corrective operation, direct closure of ASD and PDA, VSD closure with Dacron patch, Enlargement of left pulmonary artery with pericardial patch and Relief of ROTO with Rastelli procedure could be successfully performed without complication.