Journal of Korean Academy of Oral and Maxillofacial Radiology (치과방사선)

Korean Academy of Oral and Maxillofacial Radiology (대한영상치의학회)
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RADIOLOGIC STUDY OF BASAL CELL NEVUS SYNDROME

기저세포모반 증후군의 방사선학적 연구

  • Park Tae Won (Dept. of Oral Radiology, College of Dentistry, Seoul National University)
  • 박태원 (서울대학교 치과대학 치과방사선학교실)
  • Published : 1988.12.01
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Abstract

Several cases of jaw cyst-basal cell nevus-bifid rib syndrome are presented. This syndrome consists principally of multiple jaw cysts, basal cell nevi, and bifid ribs but no one component is present in all patients. The purpose of this paper is to review the multiple characteristics of this syndrome and present three cases in a family and additional 4 cases. The many malformations associated with the syndrome have variable expressivity. In the cases, multiple jaw cysts, palmar and plantar pittings, bridging of sella, temporoparietal bossing, hypertelorism, cleft palate, and dystopia canthorum have been observed.

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