Journal of Yeungnam Medical Science
- Volume 4 Issue 1
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- Pages.157-163
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- 1987
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- 2799-8010(eISSN)
Osteogenesis Imperfecta (Correction of Anterior Tibial Bowing) - A case report -
골형성 부전증환자의 경골 전방만곡 교정 치험례
- Seo, Jae-Sung (Department of Orthopedic Surgery, College of Medicine, Yeungnam University) ;
- Ihn, Joo-Chul (Department of Orthopedic Surgery, College of Medicine, Yeungnam University)
- Published : 1987.06.30
Abstract
Osteogenesis imperfecta has been categorized as a heritable disorder of connective tissue affecting both bone and soft tissues and is characterized by fragility of bone, blue sclerae, and deafness, less frequently by dentinogenesis imperfecta and laxity of ligament. The goals of orthopedic management with osteogenesis imperfecta are the treatment of acute fractures and long-term rehabilitation in an effort to maintain ambulation. We report a case of osteogenesis imperfecta with anterior bowing of tibia which was successfully corrected by multiple osteotomies and intramedullary fixation by Sofield method and reviewed literatures.
저자들은 7세 여아에서 골형성 부전증으로 우측경골에 심한 전방만곡을 절골술 및 수내고정법으로 교정하였다.
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